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Fehlbildungen der Lunge

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Kinderchirurgie

Part of the book series: Springer Reference Medizin ((SRM))

Zusammenfassung

Die wesentlichen Fehlbildungen der Lunge werden heute unter dem Begriff der „Kongenitalen thorakalen Malformationen“ (KTM) subsumiert. Unter diesem Oberbegriff werden die Congenital Pulmonary Airway Malformations (CPAM, Typ 0–4 nach Stocker), Lungensequestrationen sowie bronchogene Zysten zusammengefasst. Für symptomatische Patienten besteht die Indikation zur Resektion der KTM. Die Behandlungsoptionen für asymptomatische KMT werden kontrovers diskutiert. Zusätzlich zu den KTM sind das kongenitale lobäre Emphysem (Congenital Lobar Emphysema; CLE) und der Spontanpneumothorax, der meist aufgrund rupturierter angeborener oder erworbener Lungenbullae auftritt, für den Kinderchirurgen relevant. Die in diesem Kapitel behandelten Entitäten haben eine sehr niedrige Inzidenz. Daher ist es sinnvoll, dass die betroffenen Patienten in einem Zentrum mit fundierter kinderpneumologischer und kinderthoraxchirurgischer Expertise behandelt werden. Die Autoren halten ein interdisziplinäres Behandlungskonzept auf Grundlage der aktuellen Datenlage für essentiell.

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Author information

Authors and Affiliations

  1. Kinderchirurgische Klinik, Medizinische Hochschule Hannover, Hannover, Deutschland

    Jens Dingemann & Benno Ure

  2. Klinik für Pädiatrische Pneumologie, Allergologie und Neonatologie, Medizinische Hochschule Hannover, Hannover, Deutschland

    Nicolaus Schwerk

Authors
  1. Jens Dingemann
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  2. Nicolaus Schwerk
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  3. Benno Ure
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Corresponding author

Correspondence to Jens Dingemann .

Editor information

Editors and Affiliations

  1. Kinderchirurgische Klinik und Poliklinik, Klinikum der Universität München Kinderchirurgische Klinik und Poliklinik, München, Bayern, Germany

    Dietrich von Schweinitz

  2. Abt. Kinderchirurgie, Medizinische Hochschule Hannover (MHH) Kinderklinik, Hannover, Germany

    Benno Ure

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© 2018 Springer-Verlag GmbH Deutschland, ein Teil von Springer Nature

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Dingemann, J., Schwerk, N., Ure, B. (2018). Fehlbildungen der Lunge. In: von Schweinitz, D., Ure, B. (eds) Kinderchirurgie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-53390-1_30-1

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  • DOI: https://doi.org/10.1007/978-3-662-53390-1_30-1

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-662-53390-1

  • Online ISBN: 978-3-662-53390-1

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