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Fehlbildungen der Lunge

  • Jens Dingemann
  • Nicolaus Schwerk
  • Benno Ure
Living reference work entry
Part of the Springer Reference Medizin book series (SRM)

Zusammenfassung

Die wesentlichen Fehlbildungen der Lunge werden heute unter dem Begriff der „Kongenitalen thorakalen Malformationen“ (KTM) subsumiert. Unter diesem Oberbegriff werden die Congenital Pulmonary Airway Malformations (CPAM, Typ 0–4 nach Stocker), Lungensequestrationen sowie bronchogene Zysten zusammengefasst. Für symptomatische Patienten besteht die Indikation zur Resektion der KTM. Die Behandlungsoptionen für asymptomatische KMT werden kontrovers diskutiert. Zusätzlich zu den KTM sind das kongenitale lobäre Emphysem (Congenital Lobar Emphysema; CLE) und der Spontanpneumothorax, der meist aufgrund rupturierter angeborener oder erworbener Lungenbullae auftritt, für den Kinderchirurgen relevant. Die in diesem Kapitel behandelten Entitäten haben eine sehr niedrige Inzidenz. Daher ist es sinnvoll, dass die betroffenen Patienten in einem Zentrum mit fundierter kinderpneumologischer und kinderthoraxchirurgischer Expertise behandelt werden. Die Autoren halten ein interdisziplinäres Behandlungskonzept auf Grundlage der aktuellen Datenlage für essentiell.

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Copyright information

© Springer-Verlag GmbH Deutschland, ein Teil von Springer Nature 2018

Authors and Affiliations

  1. 1.Kinderchirurgische KlinikMedizinische Hochschule HannoverHannoverDeutschland
  2. 2.Klinik für Pädiatrische Pneumologie, Allergologie und NeonatologieMedizinische Hochschule HannoverHannoverDeutschland

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