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Craniosynostoses

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Pediatric Neuroradiology

Abstract

Craniosynostoses are serious abnormalities of infancy and childhood. The term craniosynostosis (CS) indicates a cranial or craniofacial dysmorphism characterized by the premature closure of one or more sutures of the cranial vault and/or base. Classification is based on etiology, number of involved sutures, and association with other malformations or developmental defects. Among radiological methods, thiree-dimensional computerized tomography (3DCT) plays a major role in the characterization of these disorders and in the evaluation of surgical results, with a growing role for magnetic resonance imaging (MRI) especially in patients with neurological disorders, raised intracranial pressure, or syndromic craniostenoses. This chapter highlights the pathophysiology of normal and abnormal skull growths, the rationale and indications for radiological studies, and the imaging features of the principal nonsyndromic and syndromic craniosynostoses.

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Authors and Affiliations

  1. Institute of Radiology, Universitá Cattolica del Sacro Cuore, Rome, Italy

    Gabriella D’Apolito & Cesare Colosimo

  2. Department of Neurosurgery, Istituto Giannina Gaslini, Genoa, Italy

    Armando Cama

  3. Department of Neuroradiology, Genoa, Italy

    Andrea Rossi

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  1. Gabriella D’Apolito
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  2. Cesare Colosimo
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  3. Armando Cama
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  4. Andrea Rossi
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Correspondence to Andrea Rossi .

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Editors and Affiliations

  1. Department of Neuroradiology, G Gaslini Children's Hospital, Genoa, Italy

    Andrea Rossi

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D’Apolito, G., Colosimo, C., Cama, A., Rossi, A. (2015). Craniosynostoses. In: Rossi, A. (eds) Pediatric Neuroradiology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-46258-4_61-1

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