Spermatic Cord Deep Angiomyxoma

Synonyms

Aggressive angiomyxoma

Definition

Deep angiomyxoma is a locally aggressive mesenchymal tumor composed by vascular and myxoid elements.

Clinical Features

• Incidence

  Deep angiomyxoma is a very rare tumor in male population, with fewer than 50 cases reported (Hsieh et al. 2018.

• Age

  The tumor can occur in all ages, from 1 to 82 years (Idrees et al. 2006).

• Sex

  It usually occurs in vulvovaginal region, perineum, and pelvis of women in productive age, but it is occasionally seen also in men (Hsieh et al. 2018).

• Site

  The most common site is the scrotum; other sites include the inguinal region and, occasionally, perineum, deep pelvis, spermatic cord, prostate, and epididymis (Fletcher et al. 2016; Hsieh et al. 2018; Idrees et al. 2006).

• Treatment

  Surgical excision is the treatment of choice, although achieving negative surgical margins is challenging because of the infiltrative nature of the lesion (Hsieh et al. 2018). For cases with expression of estrogen/progesterone receptor,...