Multicystic Renal Dysplasia
A nonheritable developmental disease resulting of abnormal metanephric differentiation.
It occurs in 1 in 4300 live births. Multicystic dysplastic kidneys are also a finding of genetic disorders (Sanna-Cherchi et al. 2007).
Multicystic renal dysplasia affects predominantly males.
The condition is usually unilateral.
Although previously, nephrectomy was the treatment of choice to avoid potential complications such as infection, pain, hypertension, and malignancy, to date the management is primarily conservative.
Most patients have a favorable prognosis.
Multicystic renal dysplasia is usually sporadic but may rarely be associated with obstruction, multi-malformation syndromes, chromosomal anomalies, or hereditary malformation syndromes. Unilateral multicystic renal dysplasia is the most common cause of renal mass in childhood. Bilateral lesions may be present...