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Rare Lung Diseases of Newborns

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Neonatology

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Abstract

Rare causes of respiratory distress in the newborn, mainly in term infants, need to be considered in uncommon and atypical circumstances. Embryological, pathological, surgical, antenatal, or pediatric classifications for rare lung diseases have been reported. The following is a description of rare but not negligible pulmonary diseases causing respiratory distress with neonatal presentation.

Parenchymal diseases and cystic lung diseases are briefly dealt with in order to favor the clinical approach and the diagnostic orientation in these rare and often life-threatening conditions.

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Abbreviations

ACD:

Alveolar capillary dysplasia

BC:

Bronchogenic cyst

BPS:

Bronchopulmonary sequestration

CCAM:

Congenital cystic adenomatoid malformation

CDH:

Congenital diaphragmatic hernia

CLE:

Congenital lobar emphysema

CPL:

Congenital pulmonary lymphangiectasia

PCD:

Primary ciliary dyskinesia

PPHN:

Persistent pulmonary hypertension of the newborn

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Authors and Affiliations

  1. Neonatologia e Terapia Intensiva Neonatale, Fondazione MBBM, ASST-Ospedale San Gerardo-Monza, Via Pergolesi, 33, Monza, 20900, Italy

    Paolo Tagliabue & Elena Ciarmoli

Authors
  1. Paolo Tagliabue
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  2. Elena Ciarmoli
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Corresponding author

Correspondence to Paolo Tagliabue .

Editor information

Editors and Affiliations

  1. Siena, Italy

    Giuseppe Buonocore

  2. Medicina della Riproduzione, Università di Siena Dipto. Pediatria, Ostetricia e, Siena, Italy

    Rodolfo Bracci

  3. Liverpool Women's Hospital Neonatal Unit, Liverpool, United Kingdom

    Michael Weindling

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Tagliabue, P., Ciarmoli, E. (2016). Rare Lung Diseases of Newborns. In: Buonocore, G., Bracci, R., Weindling, M. (eds) Neonatology. Springer, Cham. https://doi.org/10.1007/978-3-319-18159-2_207-1

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  • DOI: https://doi.org/10.1007/978-3-319-18159-2_207-1

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  • Publisher Name: Springer, Cham

  • Online ISBN: 978-3-319-18159-2

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