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Rare Lung Diseases of Newborns

  • Paolo Tagliabue
  • Elena Ciarmoli
Living reference work entry

Abstract

Rare causes of respiratory distress in the newborn, mainly in term infants, need to be considered in uncommon and atypical circumstances. Embryological, pathological, surgical, antenatal, or pediatric classifications for rare lung diseases have been reported. The following is a description of rare but not negligible pulmonary diseases causing respiratory distress with neonatal presentation.

Parenchymal diseases and cystic lung diseases are briefly dealt with in order to favor the clinical approach and the diagnostic orientation in these rare and often life-threatening conditions.

Keywords

Congenital Diaphragmatic Hernia Primary Ciliary Dyskinesia Pulmonary Hypoplasia Bronchogenic Cyst Congenital Cystic Adenomatoid Malformation 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Abbreviations

ACD

Alveolar capillary dysplasia

BC

Bronchogenic cyst

BPS

Bronchopulmonary sequestration

CCAM

Congenital cystic adenomatoid malformation

CDH

Congenital diaphragmatic hernia

CLE

Congenital lobar emphysema

CPL

Congenital pulmonary lymphangiectasia

PCD

Primary ciliary dyskinesia

PPHN

Persistent pulmonary hypertension of the newborn

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Copyright information

© Springer International Publishing Switzerland 2016

Authors and Affiliations

  1. 1.Neonatologia e Terapia Intensiva NeonataleFondazione MBBM, ASST-Ospedale San Gerardo-MonzaMonzaItaly

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