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Pediatric Causes of Short Bowel Syndrome

  • Myles Dworkin
  • Reto M. Baertschiger
Living reference work entry
Part of the Organ and Tissue Transplantation book series (OTT)

Abstract

Short bowel syndrome in pediatric patients can be a life threatening condition and is associated with insufficient intestinal absorptive function to sustain life without parenteral nutritional support. Causes of short bowel syndrome in children are multiple and can be secondary to congenital defects or acquired secondary to trauma inflammatory bowel disease, or other cause. The following are causes of short bowel syndrome in order of frequency: necrotizing enterocolitis, intestinal atresias, abdominal wall defects (gastroschisis and omphalocele), malrotation with midgut volvulus, Hirschsprung’s disease, trauma, and Crohn’s disease followed by rarer causes. The treatment of these conditions is surgical most of the time and aims at preserving as much bowel length as possible and allow intestinal adaptation. If this fails, small bowel transplantation may be necessary.

Keywords

Pediatric causes of short bowel syndrome Necrotizing enterocolitis Intestinal atresias Gastroschisis Omphalocele Vanishing bowel syndrome Malrotation Mid-gut volvulus Hirschsprung’s disease Crohn’s disease Trauma 

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Copyright information

© Springer International Publishing AG 2018

Authors and Affiliations

  1. 1.Thomas Jefferson UniversityPhiladelphiaUSA
  2. 2.Geisel School of Medicine at DartmouthHanoverUSA

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