Abstract
Solitary fibrous tumor (SFT) is an uncommon spindle cell tumor of mesenchymal origin. SFT was first described as a pleural-based mass, but has since been identified in numerous extra-pleural sites including the orbit. Although generally benign, malignant variants have been identified and metastasis can rarely occur [1,2,3]. Ovoid, well-circumscribed, lobulated mass on noncontrast CT that may appear heterogeneous and may contain calcifications. MRI of benign lesions shows heterogeneous iso- to hypointensity on T1w and heterogeneous hypo- to iso-intensity on T2w sequences; hyperintense signal on T1 may suggest recent hemorrhage (methemoglobin). Heterogeneous hyperintensity on T2w sequences raises the possibility of cystic degeneration or hemorrhage. Tubular flow-void signals are occasionally seen, representing intra-tumoral vessels. Marked homogeneous or heterogeneous enhancement following contrast administration may have central cystic or necrotic changes in larger or malignant lesions. Regions of restricted diffusion may be seen [1,2,3,4,5,6,7].
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Ben Cnaan, R., Karlin, J.N., Niry, D., Leibovitch, I., Goldberg, R.A. (2022). Solitary Fibrous Tumor of the Orbit. In: Ben Simon, G., Greenberg, G., Landau Prat, D. (eds) Atlas of Orbital Imaging . Springer, Cham. https://doi.org/10.1007/978-3-030-62426-2_30
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DOI: https://doi.org/10.1007/978-3-030-62426-2_30
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