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Macrodactyly

Living reference work entry

Abstract

Macrodactyly is a rare congenital anomaly resulting in overgrowth of all the mesenchymal elements of the digit including phalanges, tendons, nerves, and vessels. Currently, the term macrodystrophia lipomatosa refers to a form of progressive macrodactyly with osseous involvement associated with diffuse overgrowth of adipose tissue (Yaghmai et al. 1976; Baruchin et al. 1988; Viola et al. 1991).

Keywords

Median Nerve Rare Congenital Anomaly Digital Nerve Closing Wedge Osteotomy Proteus Syndrome 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

References

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Copyright information

© Springer Science+Business Media New York 2014

Authors and Affiliations

  1. 1.Perinatal and Clinical Genetics, Department of PediatricsLSU Health Sciences CenterShreveportUSA
  2. 2.Medical GeneticsShriners Hospitals for ChildrenShreveportUSA

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