Behçet Disease

Living reference work entry


In 1937, Behçet (1937) first described three patients with oral and genital ulceration and hypopyon. It is most common in the Middle and Far East with a prevalence of 7–8 per 100,000 people, whereas in the USA the prevalence is estimated at 4 per 1,000,000 people.


Corticosteroid Interferon Cyclosporine Meningitis Perforation 


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Copyright information

© Springer Science+Business Media New York 2016

Authors and Affiliations

  1. 1.Medical GeneticsShriners Hospitals for ChildrenShreveportUSA
  2. 2.Perinatal and Clinical Genetics, Department of PediatricsLSU Health Sciences CenterShreveportUSA

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