Abstract
Aplasia cutis congenita (ACC) is a clinical description of the absence of the skin at birth, first described by Cordon in 1767. It is a heterogeneous group of disorders characterized by absence of epidermis, dermis, and, sometimes, subcutaneous tissue, muscle, or bone on one or more parts of the body. The incidence is estimated to be 1 in 10,000 births.
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Chen, H. (2016). Aplasia Cutis Congenita. In: Atlas of Genetic Diagnosis and Counseling. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-6430-3_15-3
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DOI: https://doi.org/10.1007/978-1-4614-6430-3_15-3
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Aplasia Cutis Congenita- Published:
- 07 November 2016
DOI: https://doi.org/10.1007/978-1-4614-6430-3_15-3
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Aplasia Cutis Congenita- Published:
- 04 January 2016
DOI: https://doi.org/10.1007/978-1-4614-6430-3_15-2