Definition
Progeria syndrome is a very rare, genetic syndrome that is characterized by greatly exaggerated premature aging; an individual with progeria syndrome generally succumbs to heart attack or stroke by age 13 [6]. In more detail, progeria is a sporadically occurring, autosomal disorder meaning that only one copy of a gene is necessary for the condition [3]. To understand the basis for progeria’s occurrence, a brief summary of genetic mechanism is needed. The recipe for generating and following competent genetic instructions is relatively simple to understand. The molecule of genetic inheritance, DNA, is a string of DNA nucleotides which accords a nearly identical RNA nucleotide string. The RNA nucleotide string is itself transformed or translated into an a chain of amino acids that can become folded into a protein [2]. The alphabetical code or nucleotides for DNA and RNA are differentiated from one or the other by their chemical...
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Phelps, B.I. (2011). Progeria Syndrome. In: Goldstein, S., Naglieri, J.A. (eds) Encyclopedia of Child Behavior and Development. Springer, Boston, MA. https://doi.org/10.1007/978-0-387-79061-9_2264
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DOI: https://doi.org/10.1007/978-0-387-79061-9_2264
Publisher Name: Springer, Boston, MA
Print ISBN: 978-0-387-77579-1
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