Synonym(s)
Gottron's syndrome
Definition
Premature aging of the skin, predominately affecting the distal extremities, without other features of premature aging
Pathogenesis
Autosomal recessive inheritiance; may be related to type IV Ehlers-Danlos syndrome
Clinical manifestation
Dry, thin, wrinkled skin; most prominent over the distal extremities; dystrophic nails; short stature; normal life expenctancy
Differential diagnosis
Werner's syndrome (pangeria); progeria
Therapy
None
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References
Greally JM, Boone LY, Lenkey SG, Wenger SL, Steele MW (1992) Acrometageria: a spectrum of “premature aging” syndromes. American Journal of Medical Genetics 44(3):334–339
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© 2004 Springer-Verlag
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(2004). Acrogeria. In: Levine, N., Levine, C.C. (eds) Dermatology Therapy. A to Z Essentials. Springer, Berlin, Heidelberg. https://doi.org/10.1007/3-540-29668-9_65
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DOI: https://doi.org/10.1007/3-540-29668-9_65
Publisher Name: Springer, Berlin, Heidelberg
Print ISBN: 978-3-540-00864-4
Online ISBN: 978-3-540-29668-3
eBook Packages: Springer Book Archive