Pediatric Surgery pp 1107-1124 | Cite as

Short Bowel Syndrome

  • Michael E. HöllwarthEmail author
Reference work entry


Short bowel syndrome occurs after extensive loss of small bowel leading to a status of intestinal failure characterized by significant problems in digesting and absorbing enteral nutrition. A very complex adaptation process of the intestine allows that 90% of the patients can be weaned after a long-term period from parenteral nutrition. A small number of patients will finally need surgical interventions either to reduce a very fast passage time or to lengthen the dilated intestinal remnants. Some patients will need intestinal or combined intestinal/liver transplantation either after nearly total loss of small bowel or after severe complication such as intestinal failure-associated liver insufficiency. The therapeutic decisions have to be tailored to each individual patient depending which parts of the intestine are lost or which dysfunctions of the intestinal remnants need a special treatment. Survival rates reach today nearly 90% including some children with long-term home parenteral support, additionally to the enteral nutrition.


Short bowel syndrome Intestinal adaptation Intestinal failure Liver insufficiency Bacterial overgrowth Dysmotility Bacterial translocation Central venous line Sepsis 


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Authors and Affiliations

  1. 1.Department of Paediatric and Adolescent SurgeryMedical University of GrazGrazAustria

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