Encyclopedia of Clinical Neuropsychology

2018 Edition
| Editors: Jeffrey S. Kreutzer, John DeLuca, Bruce Caplan

Klüver-Bucy Syndrome

  • Kelly Davis Garrett
  • Farzin IraniEmail author
  • David J. Libon
  • Rod Swenson
Reference work entry
DOI: https://doi.org/10.1007/978-3-319-57111-9_1618

Synonyms

KBS; Temporal lobe syndrome

Short Description or Definition

Klüver-Bucy syndrome (KBS) is a disorder classically associated with bilateral extirpation of the temporal lobe, including most of the hippocampus and amygdala, resulting in six core symptoms: (1) visual agnosia, (2) hyperorality, (3) hypermetamorphosis, (4) alterations in emotional behavior, (5) changes in sexual behavior, and (6) changes in dietary habits. The initial work of Klüver and Bucy (1937, 1938, 1939) was important in furthering understanding of the function of the temporal lobes and associated structures, Papez’s neuroanatomic circuit of emotion (Papez 1937), as well as neurobehavioral phenomena including amnesia and agnosia. Though comparatively scarce, case descriptions of KBS are uniformly rich.

Categorization

Both partial and complete KBS involving animals and humans have been reported. Human KBS syndrome has been described in children, adolescents, and adults. Following the suggestion of Lilly,...

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References and Readings

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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  • Kelly Davis Garrett
    • 1
  • Farzin Irani
    • 2
    Email author
  • David J. Libon
    • 3
  • Rod Swenson
    • 4
  1. 1.Intermountain Healthcare and University of Utah Center on AgingSalt Lake CityUSA
  2. 2.Psychology DepartmentWest Chester University of PennsylvaniaWest ChesterUSA
  3. 3.Departments of Geriatrics, Gerontology, and PsychologyRowan University, New Jersey Institute for Successful Aging, School of Osteopathic MedicineStratfordUSA
  4. 4.Department of Psychiatry and Behavioral ScienceUniversity of North Dakota School of MedicineFargoUSA