KBS; Temporal lobe syndrome
Short Description or Definition
Klüver-Bucy syndrome (KBS) is a disorder classically associated with bilateral extirpation of the temporal lobe, including most of the hippocampus and amygdala, resulting in six core symptoms: (1) visual agnosia, (2) hyperorality, (3) hypermetamorphosis, (4) alterations in emotional behavior, (5) changes in sexual behavior, and (6) changes in dietary habits. The initial work of Klüver and Bucy (1937, 1938, 1939) was important in furthering understanding of the function of the temporal lobes and associated structures, Papez’s neuroanatomic circuit of emotion (Papez 1937), as well as neurobehavioral phenomena including amnesia and agnosia. Though comparatively scarce, case descriptions of KBS are uniformly rich.
Both partial and complete KBS involving animals and humans have been reported. Human KBS syndrome has been described in children, adolescents, and adults. Following the suggestion of Lilly,...
References and Readings
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