Encyclopedia of Clinical Neuropsychology

2018 Edition
| Editors: Jeffrey S. Kreutzer, John DeLuca, Bruce Caplan

Deaf/Hearing Impairment

  • Deborah Witsken
  • Yuan Yuan WangEmail author
Reference work entry
DOI: https://doi.org/10.1007/978-3-319-57111-9_1447

Synonyms

Deaf; Hard of hearing; Hearing impaired; Hearing loss

Short Description or Definition

Medical definitions of deafness refer to impairment in the physical structures necessary for hearing and understanding language. The term deaf refers to a degree of hearing loss that significantly impacts access to auditory language; hard of hearing typically refers to a hearing loss that still allows for some understanding of auditory information. Medical and functional definitions of deafness do not necessarily correspond with an individual’s cultural identity. The cultural definition (commonly indicated by the capitalized term “Deaf”) refers to individuals who reject the medical notion that deafness represents impairment per se and identify with a community of individuals who share common experiences, a rich cultural heritage, and a shared language – sign language (Lane et al. 1996).

Syndromes

Konigsmark and Gorlin (1976) have described over 140 syndromes of hearing loss, and the...

This is a preview of subscription content, log in to check access.

References and Readings

  1. American Speech-Language-Hearing Association (2009). The prevalence and incidence of hearing loss in children. Retrieved 11 June 2009 from http://www.asha.org/public/hearing/disorders/children.htm
  2. Black, P., & Glickman, N. (2005). Language dysfluency in the deaf inpatient population. JADARA, 39(1), 303–321.Google Scholar
  3. Black, P., & Glickman, N. (2009). Language and learning challenges in the deaf psychiatric population. In Cognitive-behavioral therapy for deaf and hearing persons with language and learning challenges (pp. 1–46). New York: Taylor & Francis.Google Scholar
  4. Braden, J. P. (1994). Deafness, deprivation, and IQ. New York: Plenum.CrossRefGoogle Scholar
  5. Brookhouser, P. E., Beauchaine, K. L., & Osberger, M. J. (1999). Management of the child with sensorineural hearing loss: Medical, surgical, hearing aids, cochlear implants. Pediatric Clinics of North America, 46(1), 121–141.PubMedCrossRefPubMedCentralGoogle Scholar
  6. Calderon, R., & Naidu, S. (2000). Further support for the benefits of early identification and intervention for children with hearing loss. The Volta Review, 100(5), 53–84.Google Scholar
  7. Cusimano, F., Martines, E., & Rizzo, C. (1991). The Jervell and Lange-Nielsen syndrome. International Journal of Pediatric Otorhinolaryngology, 22(1), 49–58.PubMedCrossRefPubMedCentralGoogle Scholar
  8. Danek, M. M., & Busby, H. (1999). Transition planning and programming: Empowerment through partnership. Washington, DC: Gallaudet University Press.Google Scholar
  9. Gausden, E., Coyle, B., Armour, J. A., Coffey, R., Grossman, A., Fraser, G. R., … & Luxon, L. M. (1997). Pendred syndrome: Evidence for genetic homogeneity and further refinement of linkage. Journal of Medical Genetics,34(2), 126–129.PubMedPubMedCentralCrossRefGoogle Scholar
  10. Hauser, P. C. (2001). Deaf readers’ phonological encoding: An electromyogram study of covert reading behaviour. Dissertation Abstracts International, 62, 4B. (UMI No. AAI3012772).Google Scholar
  11. Hauser, P. C., Wills, K., & Isquith, P. K. (2006). Hard-of-hearing, deafness, and being Deaf. In J. E. Farmer, J. Donders, & S. A. Warschausky (Eds.), Treating neurodevelopmental disabilities (pp. 119–131). New York: Guilford.Google Scholar
  12. Kenneson, A., & Cannon, M. J. (2007). Review and meta-analysis of the epidemiology of congenital cytomegalovirus (CMV) infection. Reviews in Medical Virology, 17(4), 253–276.PubMedCrossRefPubMedCentralGoogle Scholar
  13. Kochhar, A., Fischer, S. M., Kimberling, W. J., & Smith, R. J. (2007). Branchio-oto-renal syndrome. American Journal of Medical Genetics Part A, 143(14), 1671–1678.CrossRefGoogle Scholar
  14. Konings, A., Van Laer, L., Michel, S., Pawelczyk, M., Carlsson, P. I., Bondeson, M. L., … & Huyghe, J. (2009). Variations in HSP70 genes associated with noise-induced hearing loss in two independent populations. European Journal of Human Genetics, 17(3), 329–335.PubMedPubMedCentralCrossRefGoogle Scholar
  15. Konigsmark, B. W., & Gorlin, R. J. (1976). Genetic and metabolic deafness. WB Saunders Company.Google Scholar
  16. Kremer, H., van Wijk, E., Märker, T., Wolfrum, U., & Roepman, R. (2006). Usher syndrome: Molecular links of pathogenesis, proteins and pathways. Human Molecular Genetics, 15(suppl 2), R262–R270.PubMedCrossRefPubMedCentralGoogle Scholar
  17. Kruegel, J., Rubel, D., & Gross, O. (2013). Alport syndrome – Insights from basic and clinical research. Nature Reviews Nephrology, 9(3), 170–178.PubMedCrossRefPubMedCentralGoogle Scholar
  18. Lane, H. (1988). Is there a “psychology of the deaf”? Exceptional Children, 55, 7–19.PubMedCrossRefPubMedCentralGoogle Scholar
  19. Lane, H., Hoffmeister, R., & Bahan, B. J. (1996). A journey into the deaf-world. San Diego: Dawn Sign Press.Google Scholar
  20. Leigh, I., Corbett, C. A., Gutman, V., & Morere, D. A. (1996). Providing psychological services to deaf individuals: A response to new perceptions of diversity. Professional Psychology: Research and Practice, 27, 364–371.CrossRefGoogle Scholar
  21. Maller, S. J. (2003). Intellectual assessment of deaf people: A critical review of core concepts and issues. In M. Marshark & P. E. Spencer (Eds.), Oxford handbook of deaf studies, language, and education (pp. 451–463). New York: Oxford University Press.Google Scholar
  22. Maller, S. J., & Ferron, J. (1997). WISC-III factor invariance across deaf and standardization samples. Educational and Psychological Measurement, 7, 987–994.CrossRefGoogle Scholar
  23. Marscharck, M., & Hauser, P. C. (Eds.). (2009). Deaf cognition: Foundations and outcomes. New York: Oxford University Press.Google Scholar
  24. Meadow-Orlans, K. P. (1990). Research on developmental aspects of deafness. In D. E. Moores & K. P. Meadow-Orlans (Eds.), Education and developmental aspects of deafness (pp. 283–298). Washington, DC: Gallaudet University Press.Google Scholar
  25. Mendonça, R. H. F. D., Ferreira, E. L., & Abbruzzese, S. (2015). Electrophysiolocal findings in Mohr-Tranebjærg syndrome. Revista Brasileira de Oftalmologia, 74(2), 99–101.CrossRefGoogle Scholar
  26. Mertens, D. M., Sass-Lehrer, S., & Scott-Olson, K. (2000). Sensitivity in family professional relationships: Potential experiences of families with young deaf and hard of hearing children. In P. T. Spencer, C. J. Erting, & M. Marschark (Eds.), The deaf child in the family at school (pp. 133–150). Mahwah: Erlbaum.Google Scholar
  27. Mitchell, R. E., & Karchmer, M. A. (2002). Chasing the mythical ten percent: Parental hearing status of deaf and hard of hearing students in the United States. Sign Language Studies, 4, 138–163.CrossRefGoogle Scholar
  28. Newman, A. J., Bavelier, D., Corina, D., Jezzard, P., & Neville, H. J. (2002). A critical period for right hemisphere recruitment in American sign language processing. Nature Neuroscience, 5, 76–80.PubMedCrossRefPubMedCentralGoogle Scholar
  29. Paul, P. V., & Jackson, D. W. (1993). Toward a psychology of deafness. Needham Heights: Allyn & Bacon.Google Scholar
  30. Pisoni, D., Conway, C., Kronenberger, W., Horn, D. L., Karpicke, J., & Henning, S. C. (2008). Efficacy and effectiveness of cochlear implants in deaf children. In M. Marscharck & P. C. Hauser (Eds.), Deaf cognition: foundations and outcomes (pp. 52–101). New York: Oxford University Press.CrossRefGoogle Scholar
  31. Powers, A. R., Elliott, R. N., Patterson, D., & Shaw, S. (1995). Family environment and deaf and hard of hearing students with mild additional disabilities. Journal of Childhood Communication Disorders, 17, 15–19.CrossRefGoogle Scholar
  32. Pressman, L., Pipp-Siegel, S., Yoshinaga-Itano, C., & Deas, A. (1999). The relation of sensitivity to child expressive language gain in deaf and hard-of-hearing children whose caregivers are hearing. Journal of Deaf Studies and Deaf Education, 4, 294–304.PubMedCrossRefPubMedCentralGoogle Scholar
  33. Raz, Y. A. E. L. (2004). Conductive hearing loss. In C. M. Alper (Ed.), Advanced therapy of Otitis media (pp. 419–424). Hamilton: BC Decker.Google Scholar
  34. Read, A. P., & Newton, V. E. (1997). Waardenburg syndrome. Journal of Medical Genetics, 34(8), 656–665.PubMedPubMedCentralCrossRefGoogle Scholar
  35. Rhine-Kahlback, S. (2004). The assessment of developmental language differences, executive functioning, and social skills in deaf children. Unpublished doctoral dissertation, Gallaudet University, Washington, DC.Google Scholar
  36. Simeonsson, R. J., Wax, T. M., & White, K. (2001). Assessment of children who are deaf or hard of hearing. In R. Simeonsson & S. Rosenthal (Eds.), Psychological and developmental assessment: Children with disabilities and chronic conditions (pp. 248–266). New York: Guilford.Google Scholar
  37. Smith, R. J. H., Shearer, A. E., Hildebrand, M. S., & Van Camp, G. (2014). Deafness and hereditary hearing loss overview. In R. A. Pagon, T. D. Bird, C. R. Dolan, & K. Stephens (Eds.), GeneReviews. Seattle: University of Washington.Google Scholar
  38. Snead, M. P., & Yates, J. R. (1999). Clinical and molecular genetics of Stickler syndrome. Journal of Medical Genetics, 36(5), 353–359.PubMedPubMedCentralGoogle Scholar
  39. Song, M. H., Lee, K. Y., Choi, J. Y., Bok, J., & Kim, U. K. (2011). Nonsyndromic X-linked hearing loss. Frontiers in Bioscience (Elite Edition), 4, 924–933.Google Scholar
  40. Sussman, A. E., & Brauer, B. A. (1999). On being a psychotherapist with Deaf clients. In I. W. Leigh (Ed.), Psychotherapy with deaf clients from diverse groups (pp. 3–22). Washington, DC: Gallaudet University Press.Google Scholar
  41. Traxler, C. B. (2000). The Stanford achievement test, 9th edition: National norming and performance standards for deaf and hard of hearing students. Journal of Deaf Studies and Deaf Education, 5(4), 337–348.PubMedCrossRefPubMedCentralGoogle Scholar
  42. Wagner, M., Newman, L., Cameto, R., Garza, N., & Levine, P. (2005). After high school. A first look at the postschool experiences of youth with disabilities. A report from the National Longitudinal Transition Study - 2 (NLTS-2). Menlo Park, CA: SRI International. Retrieved 1 June 2009 from http://www.nlts2.org/pdfs/afterhighschool_report.pdf
  43. WHO (2005). Deafness and hearing impairment. Retrieved 11 June 2009 from http://www.who.int/mediacentre/factsheets/fs300/en/print.html
  44. Yoshinaga Itano, C., Sedey, A. L., Coulter, D. K., & Mehl, A. L. (1998). The language of early and later identified children with hearing loss. Pediatrics, 102, 1161–1171.PubMedCrossRefPubMedCentralGoogle Scholar

Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.University of Minnesota Medical SchoolMinneapolisUSA
  2. 2.Faculty of Health SciencesUniversity of MacauMacaoChina