Encyclopedia of Clinical Neuropsychology

2018 Edition
| Editors: Jeffrey S. Kreutzer, John DeLuca, Bruce Caplan

Hamartoma

  • Ethan MoitraEmail author
Reference work entry
DOI: https://doi.org/10.1007/978-3-319-57111-9_114

Definition

A rare focal malformation that resembles a neoplasm. The most common central nervous system hamartoma occurs inferior to the hypothalamus, either parahypothalamically or intrahypothalamically. Initial symptoms include precocious puberty, gelastic (laughing) seizures, and vision problems. Although hamartomas rarely invade or compress the surrounding structures significantly, secondary behavioral and cognitive problems may develop in childhood, leading to significant disability. Consequently, resection and radiosurgery are often the utilized treatment options.

Cross-References

References and Readings

  1. Feiz-Erfan, I., Rekate, H. L., Shetter, A. G., Siwanuwatn, R., Horn, E. M., & Spetzler, R. F. (2004). Surgical management of hypothalamic hamartomas. Barrow Neurological Institute Quarterly, 20, 4–12.Google Scholar

Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Department of Psychiatry and Human BehaviorBrown UniversityProvidenceUSA