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Limited Dorsal Spinal Nondisjunctional Disorders: Limited Dorsal Myeloschisis, Congenital Spinal Dermal Sinus Tract, and Mixed Lesions

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Textbook of Pediatric Neurosurgery

Abstract

Spinal dysraphic lesions due to incomplete fusion and consequent failed disjunction of a limited segment of the dorsal neural tube during primary neurulation are the subjects of this chapter. We use the term “limited dorsal spinal nondisjunctional disorders” (LDSNDs) to encompass several known varieties of such lesions, namely, limited dorsal myeloschisis (LDM), congenital spinal dermal sinus tract (CSDST), mixed lesions of the two, and other closely related complex lesions (Wang et al. 1993; Pang et al. 2013a; Eibach et al. 2017). All of these probably share a common embryogenetic mechanism and similar clinical manifestations.

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Author information

Authors and Affiliations

  1. Department of Neurosurgery, Tuen Mun Hospital, Hong Kong, China

    Sui-To Wong

  2. Department of Clinical Pathology, Tuen Mun Hospital, Hong Kong, China

    Amanda Kan

  3. University of California, Davis, CA, USA

    Dachling Pang

  4. Great Ormond Street Hospital For Children, NHS Trust, London, UK

    Dachling Pang

Authors
  1. Sui-To Wong
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  2. Amanda Kan
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  3. Dachling Pang
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Corresponding authors

Correspondence to Sui-To Wong or Dachling Pang .

Editor information

Editors and Affiliations

  1. International Neuroscience Institute, Hannover, Germany

    Concezio Di Rocco

  2. Oakland Medical Center, Oakland, CA, USA

    Dachling Pang

  3. University of Toronto Hospital for Sick Children, Toronto, ON, Canada

    James T. Rutka

Section Editor information

  1. London, CA, UK

    Dachling Pang

  2. Division of Pediatric Neurosurgery, Seoul National University Children’s Hospital, Seoul, South Korea

    Kyu-Chang Wang

  3. Division of Pediatric Neurosurgery, Seoul National University Children’s Hospital & Seoul National University College of Medicine, Seoul, South Korea

    Kyu-Chang Wang

  4. Department of Neurosurgery, Great Ormond Street Hospital, London, UK

    Dominic N. P. Thompson MB BS BSc FRCS (SN)

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Wong, ST., Kan, A., Pang, D. (2019). Limited Dorsal Spinal Nondisjunctional Disorders: Limited Dorsal Myeloschisis, Congenital Spinal Dermal Sinus Tract, and Mixed Lesions. In: Di Rocco, C., Pang, D., Rutka, J. (eds) Textbook of Pediatric Neurosurgery. Springer, Cham. https://doi.org/10.1007/978-3-319-31512-6_110-1

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  • DOI: https://doi.org/10.1007/978-3-319-31512-6_110-1

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  • Print ISBN: 978-3-319-31512-6

  • Online ISBN: 978-3-319-31512-6

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