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Disease patterns of juvenile dermatomyositis from western India

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Abstract

A retrospective assessment of clinical characteristics, complications/ associations, laboratory investigations, treatment modalities and outcome in an inceptional cohort of 22 (male-13) children with juvenile dermatomyositis (JDM) receiving treatment at Jaslok Hospital, Mumbai during 1997–2012 was performed. Mean age at diagnosis was 7.52 ± 3.99 years. Typical skin rash and muscle weakness were present in all children. Common complications included cutaneous ulcers (27.27%), dysphagia (22.72%) and calcinosis (18.18%).All patients presented with at least one of the serum muscle enzymes elevated. Absence of mortality and cardio-pulmonary complications and a monocyclic course in 72.7% of our patients are at variance from Western series.

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Authors and Affiliations

  1. Department of Pediatrics, Jaslok Hospital and Research Centre, Dr G Deshmukh Marg, Mumbai, India

    Pranav R. Chickermane, Deepali Mankad & Raju P. Khubchandani

  2. 31, Kailas Darshan, Near Kennedy Bridge, Nana Chowk, Mumbai, 400 007, India

    Raju P. Khubchandani

Authors
  1. Pranav R. Chickermane
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  2. Deepali Mankad
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  3. Raju P. Khubchandani
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Correspondence to Raju P. Khubchandani.

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Chickermane, P.R., Mankad, D. & Khubchandani, R.P. Disease patterns of juvenile dermatomyositis from western India. Indian Pediatr 50, 961–963 (2013). https://doi.org/10.1007/s13312-013-0260-4

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  • DOI: https://doi.org/10.1007/s13312-013-0260-4

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