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Extraskeletal Ewing’s Sarcoma Arising in the Larynx

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Abstract

Extraskeletal Ewing’s sarcoma (EES), or primitive neuroectodermal tumor, is an uncommon neoplasm with low incidence in the head and neck. Occurrences in the larynx are even more exceptional with only two previous reported cases of EES arising from the larynx. We report the case of a 45-year-old woman with a laryngeal Ewing’s sarcoma treated with chemotherapy with radiotherapy to follow. Here we describe the histology, molecular diagnosis and treatment of this unusual tumor.

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Authors and Affiliations

  1. Department of Pathology H179, Penn State Hershey Medical Center, Hershey, PA, 17033, USA

    Michael C. Lynch & Nicole Williams

  2. Department of Hematology/Oncology, Pennsylvania State University College of Medicine, The Penn State Hershey Medical Center, Hershey, PA, USA

    Joseph J. Drabick

  3. Department of Otolaryngology, The Penn State Hershey Medical Center, Hershey, PA, USA

    Aaron Baker & David Goldenberg

Authors
  1. Michael C. Lynch
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  2. Aaron Baker
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  3. Joseph J. Drabick
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  4. Nicole Williams
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  5. David Goldenberg
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Correspondence to Michael C. Lynch.

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Lynch, M.C., Baker, A., Drabick, J.J. et al. Extraskeletal Ewing’s Sarcoma Arising in the Larynx. Head and Neck Pathol 8, 225–228 (2014). https://doi.org/10.1007/s12105-013-0492-6

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  • DOI: https://doi.org/10.1007/s12105-013-0492-6

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