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Congenital inclusion tumours in spinal dysraphism

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Abstract

Objective

To review the presentation, diagnosis and management of children with spinal dysraphism and CIT.

Methods

It is a retrospective review of 146 children of spina bifida over 9 years (2000–2008) and details the clinical course and outcome of seven with associated congenital inclusion tumors.

Results

7/146 (4.7%) had spina bifida with CIT, 5 dermoid cysts and 2 mature teratoma. The diagnosis was missed by the primary physician even in the presence of a neurocutaneous marker. Spinal imaging with MRI was conclusive. All were managed with multilevel laminectomy, near total/total excision of the CIT and detethering of cord. Intramedullary involvement and established neurological deficits at presentation were associated with persistent deficits.

Conclusion

Early detection and comprehensive management of CIT with spinal dysraphism ensures social fecourinary continence, preserves renal function, achieves ambulation and enables patients to lead an acceptable quality of life.

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Authors and Affiliations

  1. Department of Pediatric Surgery, St. John’s National Academy of Health Sciences, Bangalore, India

    A. M. Shubha & Kanishka Das

  2. Department of Pathology, St. John’s Medical College Hospital, St. John’s National Academy of Health Sciences, Bangalore, India

    Suravi Mohanty & Isha Garg

  3. St. John’s Medical College Hospital, St. John’s National Academy of Health Sciences, Johnnagara, Bangalore, 560034, India

    Kanishka Das

Authors
  1. A. M. Shubha
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  2. Suravi Mohanty
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  3. Kanishka Das
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  4. Isha Garg
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Corresponding author

Correspondence to Kanishka Das.

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Shubha, A.M., Mohanty, S., Das, K. et al. Congenital inclusion tumours in spinal dysraphism. Indian J Pediatr 77, 167–170 (2010). https://doi.org/10.1007/s12098-009-0290-z

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  • DOI: https://doi.org/10.1007/s12098-009-0290-z

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