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Dieulafoy’s disease of the lung: a report of three cases with review of pathological aspects

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Abstract

Dieulafoy’s disease of the lung is one of the causes of cryptogenic hemoptysis often massive and recurrent, caused by dysplastic superficially located arteries in the bronchial wall. Being a rare condition, available literature on this condition is limited to a few case reports and series. We report three such cases presenting with severe hemoptysis uncontrolled by bronchial artery embolization who subsequently underwent resection of the involved lobe of the lung. The clinical, radiological, bronchoscopic, and pathological features are discussed with emphasis on the gross and microscopic characteristics that aid in the pathological diagnosis in the resected specimens.

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Acknowledgments

The authors thank Dr. Pattabhiraman. V.R, Consultant Pulmonologist, KMCH, Coimbatore for the valuable insights and bronchoscopic images.

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Authors and Affiliations

  1. Department of Pathology, Kovai Medical Center and Hospital, Avinashi Road, Coimbatore, Tamil Nadu, 641014, India

    Albina Venus, Preithy Uthamalingam & Sangita Mehta

  2. Department of Interventional Radiology, Kovai Medical Center and Hospital, Avinashi Road, Coimbatore, Tamil Nadu, 641014, India

    Barath Sitaram

Authors
  1. Albina Venus
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  2. Preithy Uthamalingam
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  3. Barath Sitaram
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  4. Sangita Mehta
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Corresponding author

Correspondence to Preithy Uthamalingam.

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This study was not funded by any authority.

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This article does not contain any studies with human participants or animals performed by any of the authors.

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The authors declare that they have no conflict of interest.

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Venus, A., Uthamalingam, P., Sitaram, B. et al. Dieulafoy’s disease of the lung: a report of three cases with review of pathological aspects. Indian J Thorac Cardiovasc Surg 32, 217–220 (2016). https://doi.org/10.1007/s12055-016-0442-5

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  • DOI: https://doi.org/10.1007/s12055-016-0442-5

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