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Periodic Fever Syndromes

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Abstract

The periodic syndromes represent a heterogeneous group of disorders that can be very difficult for practicing physicians to diagnosis and treat. This article presents an orderly approach to hyperimmunoglobulin D syndrome; tumor necrosis factor receptor-1 periodic syndrome; familial Mediterranean fever; periodic fever with aphthous stomatitis, pharyngitis, and adenitis syndrome; and cryopyrin-associated periodic syndromes by highlighting the disease presentation, diagnosis, pathogenesis, and treatment. Recent advances are also discussed.

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Authors and Affiliations

  1. Section of Allergy, Asthma, and Immunology, Children’s Mercy Hospitals and Clinics, 2401 Gillham Road, Kansas City, MO, 64108, USA

    Zachary Jacobs & Christina E. Ciaccio

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  1. Zachary Jacobs
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  2. Christina E. Ciaccio
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Correspondence to Christina E. Ciaccio.

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Jacobs, Z., Ciaccio, C.E. Periodic Fever Syndromes. Curr Allergy Asthma Rep 10, 398–404 (2010). https://doi.org/10.1007/s11882-010-0141-z

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