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Gait in children with arthrogryposis multiplex congenita

  • Original Clinical Article
  • Published:
Journal of Children's Orthopaedics

Abstract

Purpose

Lower limb contractures and muscle weakness are common in children with arthrogryposis multiplex congenita (AMC). To enhance or facilitate ambulation, orthoses may be used. The aim of this study was to describe gait pattern among individuals wearing their habitual orthotic devices.

Methods

Fifteen children with AMC, mean age 12.4 (4.3) years, with some lower limb involvement underwent 3-D gait analysis. Three groups were defined based on orthosis use; Group 1 used knee–ankle–foot orthoses with locked knee joints, Group 2 used ankle–foot orthoses or knee–ankle–foot orthoses with open knee joints and Group 3 used no orthoses.

Results

The greatest trunk and pelvis movements in all planes and the greatest hip abduction were observed in Group 1, compared to Groups 2 and 3, as well as to the gait laboratory control group. Maximum hip extension was similar in Groups 1 and 2, but in Group 3, there was less hip extension and large deviations from the control data. Lower cadence and walking speed were observed in Group 1 than in Groups 2 and 3. The step length was similar in all groups and also with respect to the gait laboratory reference values.

Conclusions

Children with AMC were subdivided according to orthoses use. Kinematic data as recorded with 3-D gait analysis showed differences among the groups in trunk, pelvis and knee kinematics, and in cadence and walking speed. The step length was similar in all groups and to the gait laboratory reference values, which may be attributable to good hip extension strength in all participants.

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Acknowledgments

We would like to thank the children and their parents for participating in the study. This study was supported by the Norrbacka-Eugenia Foundation.

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Correspondence to Åsa Bartonek.

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Eriksson, M., Gutierrez-Farewik, E.M., Broström, E. et al. Gait in children with arthrogryposis multiplex congenita. J Child Orthop 4, 21–31 (2010). https://doi.org/10.1007/s11832-009-0234-1

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  • DOI: https://doi.org/10.1007/s11832-009-0234-1

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