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Malignant transformation of orbital solitary fibrous tumor

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Abstract

Orbital solitary fibrous tumor (SFT) is a rare tumor and may recur or undergo malignant transformation without complete excision. We present a case of orbital SFT which recurred twice and underwent malignant transformation. The patient was treated with en bloc excision via a lateral orbitotomy. The postoperative histopathologic diagnosis of this case was an adult fibrosarcoma. Postoperative adjuvant radiation therapy was given. In 18 months of further follow-up, there has been no evidence of recurrence, both clinically and in regular imaging studies.

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Acknowledgments

We thank Pr. Jian Wang, M.D. (Fudan University Shanghai Cancer Center, China) for her excellent advice.

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Authors and Affiliations

  1. Department of Ophthalmology, Eye and ENT Hospital of Fudan University, Shanghai, 200031, China

    Xiangning Wang, Jiang Qian & Rui Zhang

  2. Department of Pathology, Eye and ENT Hospital of Fudan University, Shanghai, China

    Yingwen Bi

  3. Department of Pathology, Fudan University Shanghai Cancer Center, Shanghai, China

    Bo Ping

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  1. Xiangning Wang
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  2. Jiang Qian
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  3. Yingwen Bi
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  4. Bo Ping
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  5. Rui Zhang
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Correspondence to Jiang Qian.

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Wang, X., Qian, J., Bi, Y. et al. Malignant transformation of orbital solitary fibrous tumor. Int Ophthalmol 33, 299–303 (2013). https://doi.org/10.1007/s10792-012-9637-y

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  • DOI: https://doi.org/10.1007/s10792-012-9637-y

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