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Dilatation of esophageal strictures in epidermolysis bullosa patients: a single center experience

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Abstract

Esophageal stricture is one of the most common gastrointestinal complication in epidermolysis bullosa patients. We describe the technique of esophageal stricture dilatation, with a focus on safety and procedural modifications. Case series of 6 patients diagnosed with epidermolysis bullosa who underwent esophageal dilatation in our unit. Type of epidermolysis bullosa, patient’s age, dilatation technique, dysphagia free interval and complications were recorded. Four females and two males underwent a total of 31 dilatations during a 4-year follow-up. Most common dilatation technique was “through-the-scope” with three-stage baloons without radiology control, and in one case Savary bougi. Dilatation is usually done as an outpatient procedure with patients being discharged 3–4 h after the procedure. Mean dysphagia free interval is 7 months, longer is older patients. “Through-the-scope” baloons could be the best way to perform esophageal dilatation in epidermolysis bullosa patients. The procedure is short, safe with high success rate and dysphagia free interval and minimal complications.

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Acknowledgments

No financial grants of industry sponsorship for this study.

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Authors and Affiliations

  1. Endoscopy Unit, Department of Gastroenterology and Hepatology, University Hospital Center Zagreb, Kišpatićeva 12, 10000, Zagreb, Croatia

    Pave Markos, Roland Pulanic & Nadan Rustemovic

  2. Department of Anesthesiology, Clinical Hospital “Sveti Duh”, Zagreb, Croatia

    Maja Karaman

  3. Department of Dermatology and Venerology, University Hospital Center Zagreb, Zagreb, Croatia

    Slobodna Murat-Susic

  4. Department of Pediatric Gastroenterology, University Hospital Center Zagreb, Zagreb, Croatia

    Lana Omerza

Authors
  1. Pave Markos
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  2. Maja Karaman
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  3. Slobodna Murat-Susic
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  4. Lana Omerza
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  5. Roland Pulanic
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  6. Nadan Rustemovic
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Correspondence to Pave Markos.

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Our work conforms to the guidelines set forth in the Helsinki Declaration of 1975, as revised in 2000 (5), concerning Human and Animal Rights.

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The authors certify that they have no affiliations with or involvement in any organization or entity with any financial interest (such as onoraria; educational grants; participation in speakers’ bureaus; membership, employment, consultancies, stock ownership, or other equity interest; and expert testimony or patent-licensing arrangements), or non-financial interest (such as personal or professional relationships, affiliations, knowledge or beliefs) in the subject matter or materials discussed in this manuscript. Authors declare no conflict of interest.

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Markos, P., Karaman, M., Murat-Susic, S. et al. Dilatation of esophageal strictures in epidermolysis bullosa patients: a single center experience. Esophagus 13, 378–382 (2016). https://doi.org/10.1007/s10388-016-0538-4

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  • DOI: https://doi.org/10.1007/s10388-016-0538-4

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