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Simultaneous presentation of hemophagocytic syndrome and mesenteric vasculitis in a patient with systemic lupus erythematosus

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Modern Rheumatology

Abstract

We report an 18-year old female patient with systemic lupus erythematosus (SLE), who developed fever, pancytopenia, abdominal pain, and watery diarrhea. Computed tomography (CT) and bone marrow aspirate revealed lupus mesenteric vasculitis (LMV) and hemophagocytic syndrome (HPS). Serologic tests for Epstein–Barr virus (EBV) indicated its reactivation. This case demonstrates that HPS and concomitant LMV associated with viral reactivation can occur as clinical manifestations of SLE flare.

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Authors and Affiliations

  1. Division of Rheumatology, Department of Internal Medicine, School of Medicine, The Catholic University of Korea, Seoul St. Mary’s Hospital, 505 Banpo-Dong, Seocho-Gu, Seoul, 137-040, South Korea

    Su-Jin Moon, Seung-Ki Kwok, Kyung-Su Park, Sung-Hwan Park & Ho-Youn Kim

  2. Division of Rheumatology, Department of Internal Medicine, School of Medicine, The Catholic University of Korea, St. Vincent’s Hospital, 93 Chi-Dong, Suwon, 442-723, South Korea

    Wan-Uk Kim

Authors
  1. Su-Jin Moon
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  2. Seung-Ki Kwok
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  3. Kyung-Su Park
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  4. Wan-Uk Kim
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  5. Sung-Hwan Park
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Correspondence to Seung-Ki Kwok.

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Moon, SJ., Kwok, SK., Park, KS. et al. Simultaneous presentation of hemophagocytic syndrome and mesenteric vasculitis in a patient with systemic lupus erythematosus. Mod Rheumatol 21, 330–333 (2011). https://doi.org/10.1007/s10165-010-0401-8

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  • DOI: https://doi.org/10.1007/s10165-010-0401-8

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