Abstract
Myxofibrosarcoma (MFS) is a very rare fibroblast-derived sarcoma that occurs in the head and neck region. Here, we report the case of a 52-year-old man in whom MFS generated from the maxilla and whose beginning of treatment was considerably delayed because he was initially diagnosed as having a benign inflammatory lesion. Because a definite diagnosis was not obtained via 2 independent biopsies, total maxillectomy was used for both diagnosis and treatment. Histopathological and immunohistochemical analyses suggested that the tumor was a low-grade MFS. Because soft tissue tumors in the head and neck region are rare and a definite diagnosis is relatively difficult, surgical excision is indispensable if malignancy of the tumor is suspected.
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Nakahara, S., Uemura, H., Kurita, T. et al. A case of myxofibrosarcoma of the maxilla with difficulty in preoperative diagnosis. Int J Clin Oncol 17, 390–394 (2012). https://doi.org/10.1007/s10147-011-0302-7
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DOI: https://doi.org/10.1007/s10147-011-0302-7