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Juvenile polymyositis associated with ureteral necrosis: a diagnostic and therapeutic dilemma—case report and review of the literature

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Abstract

We describe an 11-year-old girl, diagnosed with juvenile polymyositis (JPM), who developed right ureteral obstruction secondary to necrosis. We emphasize the dilemmas regarding optimal timing for surgical intervention and medical treatment. Vascular involvement, which could be a part of juvenile dermatomyositis, may also be a feature of JPM. We discuss the association between vasculopathy and ureteral necrosis and review the literature regarding similar conditions. Whether the ureteral necrosis is a specific feature of vasculopathy, or a result of visceral calcinosis, needs to be further explored.

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Acknowledgments

We thank Faye Schreiber, MS for editing the manuscript.

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Authors and Affiliations

  1. Pediatric Rheumatology Unit, Department of Pediatrics, Meir Medical Center, 59 Tchernichovsky St, 4428164, Kfar Saba, Israel

    Ruby Haviv & Yosef Uziel

  2. Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel

    Ruby Haviv, Avishalom Pomeranz, Ilan Leibovitch & Yosef Uziel

  3. Pathology Department, Meir Medical Center, Kfar Saba, Israel

    Tania Zehavi

  4. Pediatric Nephrology Unit, Meir Medical Center, Kfar Saba, Israel

    Avishalom Pomeranz

  5. Department of Urology, Meir Medical Center, Kfar Saba, Israel

    Ilan Leibovitch

  6. Pediatric Urology Unit, Assaf Harofeh Medical Center, Zerifin, Be’er Ya’akov, Israel

    Amos Neheman

Authors
  1. Ruby Haviv
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  2. Tania Zehavi
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  3. Avishalom Pomeranz
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  4. Ilan Leibovitch
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  5. Amos Neheman
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  6. Yosef Uziel
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Corresponding author

Correspondence to Ruby Haviv.

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Ethical standards

This study was performed in accordance with the ethical standards laid down in the 1964 Declaration of Helsinki and its later amendments.

The patient’s parents provided informed consent to publish their daughter’s case anonymously.

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Haviv, R., Zehavi, T., Pomeranz, A. et al. Juvenile polymyositis associated with ureteral necrosis: a diagnostic and therapeutic dilemma—case report and review of the literature. Clin Rheumatol 38, 1925–1929 (2019). https://doi.org/10.1007/s10067-019-04576-4

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  • DOI: https://doi.org/10.1007/s10067-019-04576-4

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