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Tumorectomy with right thoracotomy for synchronous left atrial myxomas from Carney complex: report of a case

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Abstract

This report describes a case of synchronous left atrial myxomas from Carney complex resected through a right thoracotomy. The patient was a 30-year-old female that had previously been diagnosed with Carney complex following a genetic examination. Preoperative echocardiography showed a left atrial tumor, but intraoperative inspection revealed another tumor in the left atrium. Carney complex was first described in the 1980s and cardiac myxoma from Carney complex can occur in any cardiac chamber, presenting multiple times with postoperative recurrences, occurring at any age and without any predilection for gender, and is inherited in an autosomal-dominant manner. Treatment for cardiac myxoma from Carney complex is very important for patient mortality and morbidity and, despite the endocrine nature of the disorder, cardiologists and cardiac surgeons play an important role.

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Conflict of interest

Narihiro Ishida and the co-authors have no conflicts of interest to declare.

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Authors and Affiliations

  1. Department of General and Cardiothoracic Surgery, Graduate School of Medicine, Gifu University, 1-1 Yanagido, Gifu City, Gifu, 501-1194, Japan

    Narihiro Ishida, Katsuya Shimabukuro, Yukihiro Matsuno, Yuki Arakawa & Hirofumi Takemura

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  1. Narihiro Ishida
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  2. Katsuya Shimabukuro
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  3. Yukihiro Matsuno
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  4. Yuki Arakawa
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  5. Hirofumi Takemura
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Correspondence to Narihiro Ishida.

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Ishida, N., Shimabukuro, K., Matsuno, Y. et al. Tumorectomy with right thoracotomy for synchronous left atrial myxomas from Carney complex: report of a case. Surg Today 44, 185–187 (2014). https://doi.org/10.1007/s00595-012-0369-4

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  • DOI: https://doi.org/10.1007/s00595-012-0369-4

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