Zusammenfassung
Epitheloide Hämangioendotheliome (EHE) sind seltene Gefäßtumore, die im Allgemeinen im Weichteilgewebe entstehen. Primäre Knochen EHEs, besonders solche im Wirbelsäulenbereich, sind sehr selten. Wir präsentieren den Fall eines 30-jährigen Mannes, der mit lumbalen Schmerzen, Gehproblemen, Harninkontinenz und einem tauben Gefühl in der kaudalen Region stationär aufgenommen wurde. Die Röntgenaufnahme zeigte einen lytischen Prozess am Wirbelkörper L2 und einen Kollaps des Wirbelkörpers L1. Es wurden eine operative Entfernung des Wirbels L1 und eine totale Resektion des Tumors durchgeführt. Die histopathologische und immunhistochemische Untersuchung des Tumorgewebes unterstützte die Diagnose des EHE. In dem vorliegenden Bericht wird der nach unserem Wissen fünfte Fall eines EHE in der Wirbelsäule mit allen klinisch-pathologischen Befunden in der Literatur präsentiert.
Summary
Epithelioid hemangioendotheliomas (EHE) are rare vascular tumors which generally originate from soft tissues and visceral organs. Primary bone EHEs, especially those occurring in the spine region, are extremely rare. Our case is that of a 30-year-old man who was admitted to hospital with low back pain, difficulty in walking, post-voiding urinary incontinence and numbness in the caudal area. X-ray showed a lytic process affecting the vertebra L2 and collapse of L1. Vertebrectomy of L1 and gross total tumor resection were performed. Histopathological and immunohistochemical findings of the tumor tissue supported the diagnosis of EHE. The case, which to the best of our knowledge is only the fifth such reported case, is presented with its clinicopathological findings and a review of the literature.
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Gokhan, G., Akyuz, M., Gurer, I. et al. Epithelioid hemangioendothelioma derived from the spine region: Case report and review of the literature. Wien Klin Wochenschr 118, 358–361 (2006). https://doi.org/10.1007/s00508-006-0582-5
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DOI: https://doi.org/10.1007/s00508-006-0582-5