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A unique case of right-sided Poland syndrome with true dextrocardia and total situs inversus

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Abstract

Poland syndrome has been reported to be associated with true dextrocardia, but not with true situs inversus. In this report, we describe the first patient with total situs inversus in medical literature and try to highlight the syndrome's probable etiology and pathogenetic mechanisms in utero.

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Conflict of interest

The authors declare no conflict of interest related to this work.

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Authors and Affiliations

  1. Department of Pediatrics, Izzet Baysal Faculty of Medicine, Abant Izzet Baysal University, Golkoy, 14280, Bolu, Turkey

    Halil I. Atasoy, Taner Yavuz & Erkan Yesiller

  2. Department of Radiology, Izzet Baysal Faculty of Medicine, Abant Izzet Baysal University, Golkoy, 14280, Bolu, Turkey

    Sevil Altunrende

  3. Department of Ortopedics, Izzet Baysal Faculty of Medicine, Abant Izzet Baysal University, Golkoy, 14280, Bolu, Turkey

    Melih Guven

  4. Department of Thoracic Surgery, Izzet Baysal Faculty of Medicine, Abant Izzet Baysal University, Golkoy, 14280, Bolu, Turkey

    Ali Kılıcgun

  5. Department of Neurosurgery, Izzet Baysal Faculty of Medicine, Abant Izzet Baysal University, Golkoy, 14280, Bolu, Turkey

    Omer Polat

  6. Department of Genetics, Izzet Baysal Faculty of Medicine, Abant Izzet Baysal University, Golkoy, 14280, Bolu, Turkey

    Selma Duzenli

Authors
  1. Halil I. Atasoy
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  2. Taner Yavuz
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  3. Sevil Altunrende
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  4. Melih Guven
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  5. Ali Kılıcgun
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  6. Omer Polat
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  7. Erkan Yesiller
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  8. Selma Duzenli
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Correspondence to Halil I. Atasoy.

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Atasoy, H.I., Yavuz, T., Altunrende, S. et al. A unique case of right-sided Poland syndrome with true dextrocardia and total situs inversus. Eur J Pediatr 172, 269–272 (2013). https://doi.org/10.1007/s00431-012-1794-5

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  • DOI: https://doi.org/10.1007/s00431-012-1794-5

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