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A boy with congenital analbuminemia and steroid-sensitive idiopathic nephrotic syndrome: an experiment of nature

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Abstract

In this paper, a boy is reported with the association of congenital analbuminemia (CAA) and steroid-sensitive idiopathic nephrotic syndrome (INS), two conditions resulting independently in reduced colloid oncotic pressure. The unique occurrence helps confirm earlier reports that albumin is not the exclusive factor responsible for maintaining colloid oncotic pressure.

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Authors and Affiliations

  1. Nephrology Unit, University Children’s Hospital, Steinwiesstrasse 75, 8032, Zurich, Switzerland

    Thomas J. Neuhaus & Agnes Genewein

  2. Department of Pathology, University of Zurich, Rämistrasse 100, 8091, Zurich, Switzerland

    Thomas Stallmach

Authors
  1. Thomas J. Neuhaus
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  2. Thomas Stallmach
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  3. Agnes Genewein
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Correspondence to Thomas J. Neuhaus.

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Interest: no interest declared.

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Neuhaus, T.J., Stallmach, T. & Genewein, A. A boy with congenital analbuminemia and steroid-sensitive idiopathic nephrotic syndrome: an experiment of nature. Eur J Pediatr 167, 1073–1077 (2008). https://doi.org/10.1007/s00431-007-0620-y

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  • DOI: https://doi.org/10.1007/s00431-007-0620-y

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