Abstract
Background
Rosai-Dorfman disease (RDD) is a benign, rare, histiocytic disorder of unknown etiology. We describe the case of a 61-year-old woman who presented to the ophthalmology clinic with bilateral granulomatous anterior uveitis.
Methods
The uveitis was controlled on topical prednisolone acetate 1%. One month after presentation, she developed generalized macules and papules, and dermatologic and systemic evaluations were performed.
Results
On the basis of skin biopsy, purely cutaneous RDD was established.
Conclusion
Anterior granulomatous uveitis may be the presenting sign of cutaneous RDD. Consultation is necessary for accurate diagnosis.
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Acknowledgement
This work was supported in part by Research to Prevent Blindness, New York, NY.
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Gaviria, J.G., Johnson, D.A., Kinney, M.C. et al. Bilateral anterior granulomatous uveitis associated with cutaneous Rosai-Dorfman disease. Graefe's Arch Clin Exp Ophthalmol 243, 281–284 (2005). https://doi.org/10.1007/s00417-004-0993-9
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DOI: https://doi.org/10.1007/s00417-004-0993-9