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Extraskeletal neuroectodermal tumour of the vagina: a single case report and review

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Archives of Gynecology and Obstetrics Aims and scope Submit manuscript

Abstract

A case report and review of an extraskeletal neuroectodermal tumour of the vagina.

Background

Ewing’s sarcoma (ES) and primitive neuroectodermal tumours (PNETs) account for approximately 6–10% of primary malignant bone tumours and, following osteosarcoma, are the second most common group of bone sarcomas in children. Ewing’s sarcoma rarely affects the genitourinary tract.

Case summary

We report a rare case of extraskeletal Ewing’s sarcoma diagnosed in a 47-year-old Indian woman presenting with a simple cystic lesion in the posterior wall of the vagina. The histopathology revealed a rare presentation of a primitive malignant extraskeletal neuroectodermal tumour.

Conclusion

As our PubMed review found only six previously reported cases of vaginal extraskeletal Ewing’s sarcoma. Presentation as vaginal masses helped in early disease detection.

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Authors and Affiliations

  1. Women’s Hospital, Hamad Medical Corporation, P.O. Box. 3050, Doha, Qatar

    Halima Al-tamimi, Alia A. Al-Hadi, Al-Hareth Al-Khater, Issam Al-bozom & Najla Al-sayed

  2. Department of Histopathology, H.M.C., Doha, Qatar

    Halima Al-tamimi, Alia A. Al-Hadi, Al-Hareth Al-Khater, Issam Al-bozom & Najla Al-sayed

  3. Department of Hematology and Oncology, Al-Amal Hospital, H.M.C., Doha, Qatar

    Halima Al-tamimi, Alia A. Al-Hadi, Al-Hareth Al-Khater, Issam Al-bozom & Najla Al-sayed

Authors
  1. Halima Al-tamimi
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  2. Alia A. Al-Hadi
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  3. Al-Hareth Al-Khater
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  4. Issam Al-bozom
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  5. Najla Al-sayed
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Corresponding author

Correspondence to Alia A. Al-Hadi.

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Al-tamimi, H., Al-Hadi, A.A., Al-Khater, AH. et al. Extraskeletal neuroectodermal tumour of the vagina: a single case report and review. Arch Gynecol Obstet 280, 465–468 (2009). https://doi.org/10.1007/s00404-008-0898-7

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  • DOI: https://doi.org/10.1007/s00404-008-0898-7

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