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Low-grade fibromyxoid sarcoma, a deceptively benign tumor in a 5-year-old child

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Abstract

Low-grade fibromyxoid sarcoma (LGFMS) is very uncommon in the pediatric population with only 20% of reported cases under the age of 18. The youngest reported case to date has been in a 4-year-old child. Lesions are usually slow growing and asymptomatic, and locations described in children have included paravertebral, thigh and intrathoracic. Although benign in appearance, these lesions can behave aggressively, with local recurrence and distant metastases primarily to lungs. These lesions can be resistant to the usual chemotherapy and radiotherapy with surgical resection being the treatment of choice. We report a case of a 5-year-old boy who presented with a mass in the left buttock.

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References

  1. Evans HL (1987) Low-grade fibromyxoid sarcoma. A report of two metastasizing neoplasms having a deceptively benign appearance. Am J Surg Pathol 88(5):615–619

    CAS  Google Scholar 

  2. Evans HL (1993) Low-grade fibromyxoid sarcoma. Am J Surg Pathol 17(6):595–600

    Article  PubMed  CAS  Google Scholar 

  3. Billing SD, Giblen G, Fanburg-Smith JC (2005) Superficial low grade fibromyxoid sarcoma (Evans Tumor): a clinicopathologic analysis of 19 cases with a unique observation in the pediatric population. Am J Surg Pathol 29:204–210

    Article  Google Scholar 

  4. Canpolat C, Evans HL, Corpron C et al (1996) Fibromyxoid sarcoma in a four-year-old child: case report and review of the literature. Med Pediatr Oncol 27:561–564

    Article  PubMed  CAS  Google Scholar 

  5. Rando G, Buonuomo V, D’Urzo C et al (2005) Fibromyxoid sarcoma in a 4-year-old boy: case report and review of the literature. Pediatr Surg Int 21:311–312

    Article  PubMed  CAS  Google Scholar 

  6. Folpe AL, van den Berg E, Molenaar WM (2002) ‘Low grade fibromyxoid sarcoma’ in World Health Organization classification of tumours—pathology and genetics of tumours of soft tissue and bone. IARC Press, Lyon, pp 104–105

  7. Downs-Kelly E et al (2008) Am J Surg Pathol 32(1):8–13

    Article  PubMed  Google Scholar 

  8. Folpe AL, Lane KL, Paull G, Weiss SW (2000) Low-grade fibromyxoid sarcoma and hyalinizing spindle cell tumor with giant rosettes: a clinicopathologic study of 73 cases supporting their identity and assessing the impact of high-grade areas. Am J Surg Pathol 24:1353–1360

    Article  PubMed  CAS  Google Scholar 

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Acknowledgments

The authors thank Paul Oei, Laboratory Director/Managing Director Innovative Genetic Diagnosis NZ (IGENZ) laboratory, Auckland and Dr. Amanda Charlton, Staff Specialist, Histopathology Department, The Children’s Hospital at Westmead.

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Authors and Affiliations

  1. Department of Surgery, The Children’s Hospital at Westmead, Sydney, Australia

    Seema Menon & Ralph Cohen

  2. Department of Histopathology, The Children’s Hospital at Westmead, Sydney, Australia

    Michael Krivanek

Authors
  1. Seema Menon
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  2. Michael Krivanek
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  3. Ralph Cohen
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Correspondence to Seema Menon.

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Menon, S., Krivanek, M. & Cohen, R. Low-grade fibromyxoid sarcoma, a deceptively benign tumor in a 5-year-old child. Pediatr Surg Int 28, 211–213 (2012). https://doi.org/10.1007/s00383-011-3024-z

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  • DOI: https://doi.org/10.1007/s00383-011-3024-z

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