Skip to main content
SpringerLink
Log in

Situs inversus abdominus in association with congenital duodenal obstruction: a report of two cases and review of the literature

  • Case Report
  • Published:
Pediatric Surgery International Aims and scope Submit manuscript

Abstract

This report describes two newborns with persistent bile-stained vomiting. Their radiological investigations revealed the existence of situs inversus and duodenal obstruction. In one, the duodenal obstruction was partial, secondary to a duodenal diaphragm with a central aperture, whereas the other child had complete duodenal atresia as well as Fallot’s tetralogy. Such an association is extremely rare, with only 18 cases reported so far in the literature. Embryological aspects, investigations, and treatment are also discussed.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Log in via an institution

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Institutional subscriptions

Fig. 1
Fig. 2

References

  1. Ruben DG, Templeton MY, Ziegler MM (1983) Situs inversus: the complex inducing neonatal intestinal obstruction. J Pediatr Surg 18:751–756

    Article  PubMed  CAS  Google Scholar 

  2. Gray SW, Skandalakis JE (1972) Body asymmetry and splenic anomalies. In: Gray SW, Skandalakis JE (eds) Embryology for surgeons. Saunders, Philadelphia, pp 877–895

  3. Chacko KA, Krishnaswami S, Sukumar IP, Cherian G (1983) Isolated levocardia: two cases with abdominal situs inversus, thoracic situs solitus, and normal circulation. Am Heart J 106:155–159

    Article  PubMed  CAS  Google Scholar 

  4. Chang J, Brueckner M, Touloukian RJ (1993) Intestinal rotation and fixation abnormalities in heterotaxia: early detection and management. J Pediatr Surg 28:1281–1285

    Article  PubMed  CAS  Google Scholar 

  5. Davenport M, Savage M, Mowat AP, Howard ER (1993) Biliary atresia splenic malformation syndrome: an etiologic and prognostic subgroup. Surgery 113:662–668

    PubMed  CAS  Google Scholar 

  6. Debo Adeyemi S (1988) Combination of annular pancreas and partial situs inversus: a multiple organ malrotation syndrome associated with duodenal obstruction. J Pediatr Surg 23:188–191

    Article  PubMed  Google Scholar 

  7. Fonkalsrud E, Tompkins R, Clatworthy W (1966) Abdominal manifestations of situs inversus in infants and children. Arch Surg 92:791–795

    PubMed  CAS  Google Scholar 

  8. Iuchtman M, Golan Y, Heldenberg D, Kessler F (1933) Situs inversus abdominus in association with duodenal obstruction and internal hernia. Am J Perinatol 10:255–257

    Google Scholar 

  9. Ruben GD, Templeton J Jr, Ziegler MM (1983) Situs inversus: the complex inducing neonatal intestinal obstruction. J Pediatr Surg 18:751–756

    Article  PubMed  CAS  Google Scholar 

  10. Trytfonas GI, Chaidos C, Artzoglou PP, et al (1942) Partial situs inversus: duodenal obstruction in a neonate with isolated levocardia. J Pediatr Surg 27:1584–1586

    Article  Google Scholar 

  11. Akel S, Halabi J, Shawis R (1998) Abdominal situs inversus with congenital duodenal stenosis: rare association. Eur J Pediatr Surg 8:55–57

    Article  PubMed  CAS  Google Scholar 

  12. Mordehai J, Cohen Z, Kurzbart E, Mares AJ (2002) Preduodenal portal vein causing duodenal obstruction associated with situ inversus, intestinal malrotation, and polysplenia: a case report. J Pediatr Surg 27:1–3

    Google Scholar 

  13. Chandran H, Upadhyaya V, Pease PWB (1999) Multiple organ malrotation syndrome with duodenal atresia: a case report. Pediatr Surg Int 15:61–62

    Article  PubMed  CAS  Google Scholar 

  14. Cte F, Gagnon J (1999) Answer to case of the month #61. Situs inversus abdominis with duodenal diaphragm and intestinal malrotation. Can Assoc Radiol J 50:3202–3204

    Google Scholar 

  15. Kishan J, Bhargava RK, Kalani BP, Elzouki AY, Mir NA (1985) Situs inversus abdominis with intestinal atresia. Indian Pediatr 22:384–387

    PubMed  CAS  Google Scholar 

  16. Ziv Y, Lombrozo R, Dintsman M (1986) Preduodenal portal vein with situs inversus and duodenal atresia. Aust Paediatr J 22:69–70

    PubMed  CAS  Google Scholar 

  17. Bailey PV, Tracy TF, Connors RH Jr, Monney DP, Lewis JE, Weber TR (1993) Congenital duodenal obstruction: a 32-year review. J Pediatr Surg 28:92–95

    Article  PubMed  CAS  Google Scholar 

  18. Akhtar J, Guiney EJ (1992) Congenital duodenal obstruction. Br J Surg 79:133–135

    Article  PubMed  CAS  Google Scholar 

  19. LeWald LT (1925) Complete transposition of the viscera. A report of twenty-nine cases, with remarks on etiology. JAMA 84:216–268

    Google Scholar 

  20. Kluth D, Jaeschke-Melli S, Fiegel H (2003) The embryology gut rotation. Semin Pediatr Surg 12(4):275–279

    Article  PubMed  CAS  Google Scholar 

  21. Feitz R, Vos A (1997) Malrotation: the postoperative period. J Pediatr Surg 32:1322–1324

    Article  PubMed  CAS  Google Scholar 

Download references

Author information

Author notes

  1. Ahmed H. Al Salem

    Present address: , P.O. Box 61015, Qatif, 31911, Saudi Arabia

Authors and Affiliations

  1. Division of Pediatric Surgery, Department of Surgery, Tawam Hospital, Al Ain, Abu Dhabi, United Arab Emirates

    Akhtar Nawaz, Hilal Matta, Mustafa Hamchou, Alic Jacobez & Ahmed H. Al Salem

  2. Division of Pediatric Surgery, Department of Pediatrics, Tawam Hospital, Al Ain, Abu Dhabi, United Arab Emirates

    Omar Trad

Authors
  1. Akhtar Nawaz
    View author publications

    You can also search for this author in PubMed Google Scholar

  2. Hilal Matta
    View author publications

    You can also search for this author in PubMed Google Scholar

  3. Mustafa Hamchou
    View author publications

    You can also search for this author in PubMed Google Scholar

  4. Alic Jacobez
    View author publications

    You can also search for this author in PubMed Google Scholar

  5. Omar Trad
    View author publications

    You can also search for this author in PubMed Google Scholar

  6. Ahmed H. Al Salem
    View author publications

    You can also search for this author in PubMed Google Scholar

Corresponding author

Correspondence to Ahmed H. Al Salem.

Rights and permissions

Reprints and permissions

About this article

Cite this article

Nawaz, A., Matta, H., Hamchou, M. et al. Situs inversus abdominus in association with congenital duodenal obstruction: a report of two cases and review of the literature. Ped Surgery Int 21, 589–592 (2005). https://doi.org/10.1007/s00383-005-1412-y

Download citation

  • Accepted:

  • Published:

  • Issue Date:

  • DOI: https://doi.org/10.1007/s00383-005-1412-y

Keywords

Search

Navigation