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Long-term outcomes of anorectal malformations

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Abstract

Anorectal malformations (ARMs) and cloacal anomalies are rare and complex malformations of the lower gastrointestinal and genitourinary tracts. They affect approximately 1 in 3,500 live births. The treatment of these patients has traditionally focused on achieving urinary and faecal continence, with preservation of renal function. With improved surgical techniques and paediatric intensive care facilities, these patients now live relatively normal lives, with a near-normal life expectancy. Comparing results reported by different surgeons is difficult because a wide range of terminology is employed to describe the anomalies encountered. This paper attempts to simplify some of the reported outcomes of bowel function to allow a more direct comparison between groups. Urinary outcomes were not so easily comparable due to the disparity in assessing patient outcomes. Therefore, before a global analysis of all groups can take place, a standardised terminology will be necessary. At present there is a gap in the published literature of comprehensive follow-up in this group of patients, particularly regarding reproductive and sexual functioning. More detailed information on long-term outcomes is needed in these patients to facilitate informed decision-making by the primary physician (usually the paediatric surgeon) and the parents on behalf of their child.

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Authors and Affiliations

  1. Academic Department of Obstetrics and Gynaecology, University College London, 86-96 Chenies Mews, London, WC1E 6HX, UK

    Melissa C Davies

  2. Elizabeth Garrett Anderson and Obstetric Hospital, University College Hospitals London, Huntley Street, London, WC1E 6AU, UK

    Sarah M Creighton

  3. Great Ormond Street Hospital, Great Ormond Street, London, WC1N 3JU, UK

    Duncan T Wilcox

Authors
  1. Melissa C Davies
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  2. Sarah M Creighton
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  3. Duncan T Wilcox
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Correspondence to Melissa C Davies.

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Davies, M.C., Creighton, S.M. & Wilcox, D.T. Long-term outcomes of anorectal malformations. Ped Surgery Int 20, 567–572 (2004). https://doi.org/10.1007/s00383-004-1231-6

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  • DOI: https://doi.org/10.1007/s00383-004-1231-6

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