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Pleuropulmonary blastoma in childhood. A malignant degeneration of pulmonary cysts

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Abstract

Pleuropulmonary blastoma (PPB) is an extremely rare intrathoracic neoplasm of early childhood with an unfavorable outcome. In this article, two children with PPB associated with pre-existing pulmonary cysts are presented. It is emphasized that surgical excision is the treatment of choice for all pulmonary cysts.

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Acknowledgements

The authors thank Dr. C. Michail-Stranzis, MD, for her helpful comments on the histopathological and immunohistochemical findings.

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Authors and Affiliations

  1. Second Department of Propedeutic Surgery, Division of Thoracic Surgery, Laikon General Hospital, Athens University School of Medicine, Athens, Greece

    T. Dosios & S. Spyrakos

  2. Department of Pediatric Cardiothoracic Surgery, Agia Sophia Children’s Hospital, Athens, Greece

    J. Stinios

  3. First Pediatric Surgery Department, , P. and A. Kyriakou Children’s Hospital, Athens University, Athens, Greece

    P. Nicolaides & E. Androulakakis

  4. Second Pediatric Department, P. and A. Kyriakou Children’s Hospital, Athens University, Athens, Greece

    A. Constantopoulos

  5. 2 Chatzigianni Mexi Str., 11528 , Athens, Greece

    T. Dosios

Authors
  1. T. Dosios
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  2. J. Stinios
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  3. P. Nicolaides
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  4. S. Spyrakos
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  5. E. Androulakakis
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  6. A. Constantopoulos
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Correspondence to T. Dosios.

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Dosios, T., Stinios, J., Nicolaides, P. et al. Pleuropulmonary blastoma in childhood. A malignant degeneration of pulmonary cysts. Ped Surgery Int 20, 863–865 (2004). https://doi.org/10.1007/s00383-003-0997-2

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  • DOI: https://doi.org/10.1007/s00383-003-0997-2

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