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A rare case of pediatric moyamoya disease with reversible white matter lesions in a 3-year-old Chinese girl

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Abstract

Moyamoya disease is a chronic cerebral vascular disease characterized by progressive occlusion of the cerebral arteries and resulting in the development of abnormal collateral circulation. We report a case of moyamoya disease in a 3-year-old Chinese girl with partly reversible white matter lesions. This case indicates that, in pediatric moyamoya disease, white matter lesions may be associated with cerebral ischemia, and they may be reversible after treatment.

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Abbreviations

MMD:

Moyamoya disease

MRA:

magnetic resonance angiography

DSA:

digital substraction angiography

DWI:

diffusion-weighted imaging

MRI:

magnetic resonance imaging

FLAIR:

fluid attenuated inversion recovery

SWI:

susceptibility-weighted imaging

MRS:

magnetic resonance spectroscopy

CBF:

cerebral blood flow

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Authors and Affiliations

  1. Department of Pediatrics, the Second Xiangya Hospital, Central South University, Changsha, 410011, Hunan, China

    Shi-Jun Li, Jie Xiong, Yang-Yang Xiao, Ding-An Mao & Li-Qun Liu

  2. Department of Radiology, the Second Xiangya Hospital, Central South University, Changsha, 410011, Hunan, China

    Yu He

Authors
  1. Shi-Jun Li
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  2. Jie Xiong
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  3. Yu He
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  4. Yang-Yang Xiao
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Correspondence to Li-Qun Liu.

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Li, SJ., Xiong, J., He, Y. et al. A rare case of pediatric moyamoya disease with reversible white matter lesions in a 3-year-old Chinese girl. Childs Nerv Syst 36, 197–201 (2020). https://doi.org/10.1007/s00381-019-04391-x

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  • DOI: https://doi.org/10.1007/s00381-019-04391-x

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