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The Chiari 3.5 malformation: a review of the only reported case

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Abstract

Introduction

In 1894, Giuseppe Muscatello described what we believe to be the only case of an occipitocervical encephalocele with a communication to the stomach. This case and its history and context compared to the Chiari 3 malformation as described 3 years earlier by Hans Chiari are presented.

Conclusions

Based on the uniqueness of this case, we propose the term Chiari 3.5 malformation be used to describe its anatomical derailment.

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Author information

Authors and Affiliations

  1. Swedish Neuroscience Institute, Swedish Medical Center, Seattle, WA, USA

    Christian Fisahn & Rod J. Oskouian

  2. Seattle Science Foundation, Seattle, WA, USA

    Christian Fisahn & R. Shane Tubbs

  3. Pediatric Neurosurgery, Children’s of Alabama, Birmingham, AL, USA

    Mohammadali M. Shoja & W. Jerry Oakes

  4. Department of Neurosurgery, Adnan Menderes University School of Medicine, Aydın, Turkey

    Mehmet Turgut

Authors
  1. Christian Fisahn
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  2. Mohammadali M. Shoja
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  3. Mehmet Turgut
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  4. Rod J. Oskouian
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  5. W. Jerry Oakes
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  6. R. Shane Tubbs
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Corresponding author

Correspondence to R. Shane Tubbs.

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The authors have no conflict of interest.

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Fisahn, C., Shoja, M.M., Turgut, M. et al. The Chiari 3.5 malformation: a review of the only reported case. Childs Nerv Syst 32, 2317–2319 (2016). https://doi.org/10.1007/s00381-016-3255-3

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  • DOI: https://doi.org/10.1007/s00381-016-3255-3

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