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Atypical neurocytoma of the spinal cord in a young child

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Abstract

Background

Extraventricular neurocytoma is a well-established entity, and non-classical sites like the cerebellum and spinal cord have occasionally been reported.

Case

We report a rare case of intramedullary neurocytoma in an 8-year-old boy who presented with paraparesis and urinary incontinence. This tumour was isointense on T1-weighted image and hyperintense on T2-weighted image, and showed heterogenous contrast enhancement.

Findings

Pathological examination showed atypical histology in the form of vascular endothelial proliferation, increased proliferation index, mitosis and necrosis.

Conclusions

Atypical location, younger age and histopathological features are some of the interesting findings in this case, which need to be documented. To the best of our knowledge, this is the youngest patient of spinal cord neurocytoma.

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Acknowledgements

The authors wish to thank Mr. Rajeshwar Khadia, Mr. Pankaj, Mrs. Kiran Rani, Mr. Anil Bisht and Mr. Gajender Singh for their technical help with the immunohistochemistry and Mr. Kamal for his secretarial assistance.

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Authors and Affiliations

  1. Institute of Pathology, ICMR, New Delhi, India

    Avninder Singh

  2. Department of Neurosurgery, Safdarjung Hospital, New Delhi, India

    Karam Chand & Hukum Singh

  3. Department of Pathology, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, 110029, India

    Chitra Sarkar & Mehar C. Sharma

Authors
  1. Avninder Singh
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  2. Karam Chand
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  3. Hukum Singh
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  4. Chitra Sarkar
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  5. Mehar C. Sharma
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Corresponding author

Correspondence to Mehar C. Sharma.

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Singh, A., Chand, K., Singh, H. et al. Atypical neurocytoma of the spinal cord in a young child. Childs Nerv Syst 23, 207–211 (2007). https://doi.org/10.1007/s00381-006-0141-4

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  • DOI: https://doi.org/10.1007/s00381-006-0141-4

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