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A case of primary Ewing’s sarcoma of the occipital bone presenting with obstructive hydrocephalus

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Abstract

Background

Ewing’s sarcomas account for approximately 10% of primary malignant bone tumors. While most of the primary Ewing’s sarcomas occur in the long bones, pelvis, or ribs, approximately 1–6% of these sarcomas arise in the skull. We found approximately 50 cases of Ewing’s sarcoma of the calvarium reported in our search of the literature. Of these, 36 cases were reported in detail.

Case report and discussion

In this article we describe a rare case of primary Ewing’s sarcoma of the occipital bone presenting with acute obstructive hydrocephalus and review the literature.

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Authors and Affiliations

  1. Department of Neurosurgery, Kansai Medical University, 10–15 Fumizono, 570-8507, Moriguchi, Osaka, Japan

    Takasumi Yasuda, Takayuki Inagaki, Yasuo Yamanouchi & Keiji Kawamoto

  2. Department of Pediatrics, Kansai Medical University, 10–15 Fumizono, 570-8507, Moriguchi, Osaka, Japan

    Urara Kohdera, Hirohide Kawasaki & Takahide Nakano

Authors
  1. Takasumi Yasuda
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  2. Takayuki Inagaki
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  3. Yasuo Yamanouchi
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  4. Keiji Kawamoto
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  5. Urara Kohdera
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  6. Hirohide Kawasaki
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  7. Takahide Nakano
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Correspondence to Takayuki Inagaki.

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Yasuda, T., Inagaki, T., Yamanouchi, Y. et al. A case of primary Ewing’s sarcoma of the occipital bone presenting with obstructive hydrocephalus. Childs Nerv Syst 19, 792–799 (2003). https://doi.org/10.1007/s00381-003-0816-z

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  • DOI: https://doi.org/10.1007/s00381-003-0816-z

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