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Urticaria and dermographism in patients with adult-onset Still’s disease

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Abstract

Adult-onset Still’s disease (AOSD) patients typically present with arthralgia, fever, lymphadenopathy and a transient salmon maculopapular rash. Only approximately 25 cases of AOSD with urticaria were described in the literature. In this article, the authors report three additional cases of AOSD with urticarial and dermographic lesions who had a good clinical response to glucocorticoid and antihistamines. A review of the literature concerning this issue is also herein written.

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Acknowledgments

JF Carvalho received grants from Federico Foundation and CNPq (300665/2009-1).

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Authors and Affiliations

  1. Department of Dermatology, Hospital das Clínicas, Sao Paulo University, Sao Paulo, Brazil

    Paulo Ricardo Criado, Liliane Akemi Ayabe, Hebert Roberto Clivati Brandt, Ricardo Romiti & Celina W. Maruta

  2. Rheumatology Division, Hospital das Clínicas, Sao Paulo University, Sao Paulo, Brazil

    Jozélio Freire de Carvalho

  3. Rua Carneiro Leão, 33 Vila Scarpelli, Santo André, São Paulo, 09050430, Brazil

    Paulo Ricardo Criado

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  1. Paulo Ricardo Criado
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  2. Jozélio Freire de Carvalho
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  3. Liliane Akemi Ayabe
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  4. Hebert Roberto Clivati Brandt
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  5. Ricardo Romiti
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  6. Celina W. Maruta
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Correspondence to Paulo Ricardo Criado.

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Criado, P.R., de Carvalho, J.F., Ayabe, L.A. et al. Urticaria and dermographism in patients with adult-onset Still’s disease. Rheumatol Int 32, 2551–2555 (2012). https://doi.org/10.1007/s00296-011-2025-5

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  • DOI: https://doi.org/10.1007/s00296-011-2025-5

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