Abstract
Wegener granulomatosis (WG) is a necrotizing granulomatous vasculitis that predominantly affects airways and kidneys. But central nervous system involvement (7–11%) is an uncommon. Massive ICH may occur in the course of WG, and this serious condition is related with high risk of mortality. Therefore, the new treatment strategies may be considered in addition to classical practices in serious organ involvement and recurrent attack. Here, we present an adult patient with WG whose disease was complicated by a massive intracerebral hemorrhage (ICH), which subsequently led to death.
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Ceri, M., Ortabozkoyun, L., Unverdi, S. et al. Massive intracerebral hemorrhage associated with Wegener granulomatosis. Rheumatol Int 32, 1813–1814 (2012). https://doi.org/10.1007/s00296-011-1954-3
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DOI: https://doi.org/10.1007/s00296-011-1954-3