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Posterior reversible encephalopathy syndrome in a patient with ANCA-associated vasculitis

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Abstract

Posterior reversible encephalopathy syndrome (PRES) is a clinical syndrome that manifests with the onset of headache, confusion or decreased level of consciousness, visual changes, and seizures in conjunction with the typical neuroimaging features of posterior cerebral white matter changes, which are usually reversible. This syndrome has been associated with hypertension, eclampsia, renal insufficiency, immunosuppressive drugs, and connective-tissue diseases. To our knowledge, only four cases of PRES associated with antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis have been reported in the literature. Here, we present a patient with ANCA-associated vasculitis complicated by PRES.

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Correspondence to Alexandra Gonzalez Fuentes.

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Fuentes, A.G., Komarla, A. & Gomez, J.I. Posterior reversible encephalopathy syndrome in a patient with ANCA-associated vasculitis. Rheumatol Int 32, 2529–2530 (2012). https://doi.org/10.1007/s00296-010-1367-8

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  • DOI: https://doi.org/10.1007/s00296-010-1367-8

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