Abstract
Acquired amegakaryocytic thrombocytopenia (AAT) is a rare disorder, characterized by severe thrombocytopenia and selective, marked decrease or absence of megakaryocytes in the bone marrow. We describe a 29-year-old female with adult onset Still’s disease preceding a diagnosis of AAT and autoimmune hemolytic anemia, which was successfully treated with cyclosporine. This is the first case of AAT in a patient with adult onset Still’s disease.
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Her, MY., Kim, TH., Chang, HK. et al. Successful treatment of acquired amegakaryocytic thrombocytopenia with cyclosporine in adult onset Still’s disease. Rheumatol Int 27, 295–298 (2007). https://doi.org/10.1007/s00296-006-0202-8
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DOI: https://doi.org/10.1007/s00296-006-0202-8