Abstract
Klippel-Trenaunay syndrome (KTS) is a rare congenital vascular disease of unknown etiology that affects one or more limbs. It is characterized clinically by three physical findings (the so-called triad): port-wine stain hemangioma, hypertrophy of the bony and/or soft tissue, and varicose veins. A review of the medical literature in 1999 revealed about 1,000 case studies. We present here the case of a patient with clinical diagnosis of KTS studied using peripheral magnetic resonance angiography.
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Fontana, A., Olivetti, L. Peripheral MR Angiography of Klippel-Trenaunay Syndrome. CVIR 27, 297–299 (2004). https://doi.org/10.1007/s00270-003-0196-5
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DOI: https://doi.org/10.1007/s00270-003-0196-5