Skip to main content
SpringerLink
Log in

Custom-made covered transjugular intrahepatic portosystemic shunt (TIPS) in an infant with trisomy 22 and biliary atresia

  • Case Report
  • Published:
Pediatric Radiology Aims and scope Submit manuscript

Abstract

We report an 8-month-old girl with portal hypertension secondary to biliary atresia. The decision to treat with TIPS was made at the age of 8 months due to recurrent variceal bleeding. The procedure was carried out with a 6-mm bare stent due to her small size. Radiological follow-up with Doppler US showed gradual stenosis and finally occlusion of the stent 80 days after implantation. Revision was performed with placement of an additional 6-mm expanded polytetrafluoroethylene (e-PTFE) stent-graft that had remained patent for 9 months, proving that in small children with a portal vein diameter less than 8 mm, the combination of a bare stent and stent-graft can provide excellent results.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Log in via an institution

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Institutional subscriptions

Fig. 1
Fig. 2
Fig. 3
Fig. 4

Similar content being viewed by others

References

  1. Rossi P, Salvatori FM, Fanelli F et al (2004) Polytetrafluoroethylene-covered nitinol stent-graft for transjugular intrahepatic portosystemic shunt creation: 3-year experience. Radiology 231:820–830

    Article  PubMed  Google Scholar 

  2. Mermuys K, Maleux G, Heye S et al (2008) Use of Viatorr expanded polytetrafluoroethylene-covered stent-graft for transjugular intrahepatic portosystemic shunt creation in children: initial clinical experience. Cardiovasc Intervent Radiol 31:S192–S196

    Article  PubMed  Google Scholar 

  3. Huppert PE, Geoffette P, Astfalk W et al (2002) Transjugular intrahepatic portosystemic shunts in children with biliary atresia. Cardiovasc Intervent Radiol 25:484–493

    Article  PubMed  Google Scholar 

  4. Riggio O, Angeloni S, Salvatori FM et al (2008) Incidence, natural history, and risk factors of hepatic encephalopathy after transjugular intrahepatic portosystemic shunt with polytetrafluoroethylene-covered stent grafts. Am J Gastroenterol 103:2738–2746

    Article  PubMed  Google Scholar 

  5. Tripathi D, Ferguson J, Barkell H et al (2006) Improved clinical outcome with transjugular intrahepatic portosystemic stent-shunt utilizing polytetrafluoroethylene covered stents. Eur J Gastroenterol Hepatol 18:225–232

    Article  Google Scholar 

  6. Boyvat F, Cekrige S, Balkanci F et al (1999) Treatment of a TIPS-biliary fistula by stent graft in a 9-year-old boy. Cardiovasc Intervent Radiol 22:67–68

    Article  PubMed  CAS  Google Scholar 

  7. Allotey J, Lacaille F, Lees M et al (2008) Congenital bile duct anomalies (biliary atresia) and chromosome 22 aneuploidy. J Pediatr Surg 43:1736–1740

    Article  PubMed  Google Scholar 

  8. Kimura T, Hasegawa T, Oue T et al (2000) Transjugular intrahepatic portosystemic shunt performed in a 2-year-old infant with uncontrollable intestinal bleeding. J Pediatr Surg 35:1597–1599

    Article  PubMed  CAS  Google Scholar 

Download references

Author information

Authors and Affiliations

  1. Department of Paediatric Radiology, Bicêtre Hospital University Paris XI, Assistance Publique Hôpitaux de Paris, 78 rue du General Leclerc, Le Kremlin-Bicetre, Cedex 94275, Paris, France

    Chrysanthi Emmanouil Chlapoutaki, Stephanie Franchi-Abella & Daniele Pariente

  2. Pediatric Hepatology and National Reference Center for Biliary Atresia, Bicêtre Hospital University Paris XI, Assistance Publique Hôpitaux de Paris, Paris, France

    Dalila Habes

Authors
  1. Chrysanthi Emmanouil Chlapoutaki
    View author publications

    You can also search for this author in PubMed Google Scholar

  2. Stephanie Franchi-Abella
    View author publications

    You can also search for this author in PubMed Google Scholar

  3. Dalila Habes
    View author publications

    You can also search for this author in PubMed Google Scholar

  4. Daniele Pariente
    View author publications

    You can also search for this author in PubMed Google Scholar

Corresponding author

Correspondence to Chrysanthi Emmanouil Chlapoutaki.

Rights and permissions

Reprints and permissions

About this article

Cite this article

Chlapoutaki, C.E., Franchi-Abella, S., Habes, D. et al. Custom-made covered transjugular intrahepatic portosystemic shunt (TIPS) in an infant with trisomy 22 and biliary atresia. Pediatr Radiol 39, 739–742 (2009). https://doi.org/10.1007/s00247-009-1211-z

Download citation

  • Received:

  • Revised:

  • Accepted:

  • Published:

  • Issue Date:

  • DOI: https://doi.org/10.1007/s00247-009-1211-z

Keywords

Search

Navigation