Abstract
A 2-week-old female infant presented with acute decompensated left ventricular failure. Echocardiography diagnosed left ventricular noncompaction cardiomyopathy with dilated phenotype and a left ventricular shortening fraction <10%. The infant was mechanically ventilated for 2 weeks and then successfully extubated. She was maintained on intravenous milrinone for 6 months until she underwent successful orthotopic heart transplantation. Young children can be supported with inotropes for prolonged periods while awaiting heart transplantation.
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McMahon, C., Murchan, H., Prendiville, T. et al. Long-Term Support with Milrinone Prior to Cardiac Transplantation in a Neonate with Left Ventricular Noncompaction Cardiomyopathy. Pediatr Cardiol 28, 317–318 (2007). https://doi.org/10.1007/s00246-007-0020-0
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DOI: https://doi.org/10.1007/s00246-007-0020-0